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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Triplet expansion disease
Anti-acetylcholine receptor antibodies
Biopsies humaines
Intercellular communication
Exon-skipping
Dysferlinopathy
Myopathy
CS
Pharyngeal muscle
Muscle
Duchenne muscular dystrophy
Muscle stem cells
Transcriptomics
Antiserum
Accelerometry
ARN
Aggregate
DNA methylation
Sarcopenia
Andermann syndrome
PABPN1
BINDING SPECIFICITY
Human
Regeneration
Geriatric assessment
Fibrosis
Antisens oligonucleotides
Arbovirus
FAPs
GENE
Skeletal muscle
Bioinformatique
Nuclear envelope
Pax7
Satellite cell
Anti-fibrotic pharmacotherapies
Differentiation
Autologous
RNA
Gene therapy
AAV vectors
Bile salt hydrolases
Xenograft
MUTATIONS
C2 domains
Oculopharyngeal muscular dystrophy
DUX4
Autoimmune diseases
Gene replacement
Annexin A2
Aged
Atrophy
Myopathies
Myogenesis
Muscle dystrophy
AChR antibodies
Dystrophie musculaire oculopharyngée
Dystrophin
CD49d
OPMD
Myoblasts
PABPN1 agregates
Aav-U7
Satellite cells
Biomarker
Alzheimer's disease
AAV
Haploinsufficiency
Neuromuscular junction NMJ
FSHD
Functional genomics
Cross-bridge kinetics
Botulinum neurotoxin
Inflammation
Metabolism
C2C12 cells
DMD
Adipose tissue
Myosin
Myoblast
2-D PAGE
Muscle fibrosis
Bioinformatics
APOPTOSIS
Thérapie génique
Actin
Cell therapy
Alphavirus
Muscle strength
Calcium
Myositis
CNOT6L
AUTOPHAGY
Agrégats de PABPN1
ALS
Dysferlin
Myotube
Lamins
Ageing
Akt